RecruitingPhase 1Phase 2NCT06053814

NS-050/NCNP-03 in Boys With DMD (Meteor50)

A Phase 1/2, First in Human, Multiple-dose, 2-part Study to Assess the Safety, Tolerability, Pharmacokinetics, and Pharmacodynamics of NS-050/NCNP-03 in Boys With Duchenne Muscular Dystrophy (DMD)


Sponsor

NS Pharma, Inc.

Enrollment

20 participants

Start Date

Sep 18, 2024

Study Type

INTERVENTIONAL

Conditions

Summary

This is a Phase 1/2 study of Multiple-Ascending Dose (MAD) levels for 12 weeks of treatment followed by 24 weeks of open-label treatment with a selected dose of NS-050/NCNP-03 administered once weekly to ambulant boys with DMD, who have a DMD exon deletion amenable to exon 50 skipping.


Eligibility

Sex: MALEMin Age: 4 YearsMax Age: 14 Years

Inclusion Criteria5

  • Male ≥ 4 years and <15 years of age;
  • Confirmed DMD exon deletion in the dystrophin gene that is amenable to skipping of exon 50 to restore the dystrophin mRNA reading frame;
  • Able to walk independently without assistive devices;
  • Able to complete the TTSTAND without assistance in <20 seconds;
  • Stable dose of glucocorticoid for at least 3 months and the dose is expected to remain on a stable dose for the duration of the study.

Exclusion Criteria5

  • Evidence of symptomatic cardiomyopathy;
  • Current or previous treatment with anabolic steroids (e.g., oxendolone, oxandrolone) or products containing resveratrol or adenosine triphosphate within 3 months prior to first dose of study drug;
  • Currently taking another investigational drug or has taken another investigational drug within 3 months prior to the first dose of study drug;
  • Surgery within the 3 months prior to the first dose of study drug or planned during the study duration;
  • Having taken any gene therapy.

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Interventions

DRUGNS-050/NCNP-03

NS-050/NCNP-03 solution for IV infusion.

DRUGPlacebo

NS-050/NCNP-03 placebo-matching solution for IV infusion.


Locations(18)

Children's Hospital Los Angeles

Los Angeles, California, United States

Children's Hospital Colorado

Aurora, Colorado, United States

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, United States

University of Kansas Medical Center

Kansas City, Kansas, United States

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States

Alberta Children's Hospital

Calgary, Alberta, Canada

British Columbia Children's Hospital

Vancouver, British Columbia, Canada

London Health Sciences Centre

London, Ontario, Canada

National Hospital Organization Nagara Medical Center

Nagara, Gifu, Japan

Hyogo Medical University Hospital

Nishinomiya, Hyōgo, Japan

NHO Osaka Toneyama Medical Center

Toyonaka, Osaka, Japan

National Center of Neurology and Psychiatry

Kodaira, Tokyo, Japan

Pusan National University Yangsan Hospital

Yangsan, Gyeongsangnam-do, South Korea

Seoul National University Hospital

Seoul, South Korea

Ankara Bilkent City Hospital

Ankara, Turkey (Türkiye)

Istanbul University

Istanbul, Turkey (Türkiye)

Yeditepe University Kosuyolu Hospital

Istanbul, Turkey (Türkiye)

View Full Details on ClinicalTrials.gov

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NCT06053814


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