RecruitingNot ApplicableNCT06188689

Evaluation of A Clinical Diagnostic Test for CRDS

Evaluation of a Clinical Diagnostic Test for Calcium Release Deficiency Syndrome: The DIAGNOSE CRDS Study


Sponsor

Population Health Research Institute

Enrollment

400 participants

Start Date

Feb 2, 2023

Study Type

INTERVENTIONAL

Conditions

Summary

Calcium Release Deficiency Syndrome (CRDS) is a novel inherited arrhythmia syndrome secondary to RyR2 loss-of-function that confers a risk of sudden cardiac death. Diagnosis of CRDS presently requires cellular-based in vitro confirmation that an RyR2 variant causes loss-of-function. We hypothesize that CRDS can be diagnosed clinically through evaluation of the repolarization response to brief tachycardia, mediated by cardiac pacing, and a subsequent pause.


Eligibility

Plain Language Summary

Simplified for easier understanding

This clinical trial is studying Pacing for people with calcium release deficiency syndrome (crds). The study is currently recruiting participants at 19 locations.

This summary was AI-generated to explain the trial in plain language. It is not medical advice. Always discuss eligibility with your doctor before enrolling in a clinical trial.

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Interventions

DIAGNOSTIC_TESTPacing

1. Ventricular 10 beat burst at 500ms (120bpm) 2. Ventricular 10 beat burst at 400ms (150bpm) 3. Atrial 10 beat burst at 500ms (120bpm) 4. Atrial 10 beat burst at 400ms (150bpm).


Locations(20)

University of California

San Francisco, California, United States

Boston Children's Hospital

Boston, Massachusetts, United States

Mayo Clinic

Rochester, Minnesota, United States

University of Washington

Seattle, Washington, United States

Antwerp University Hospital

Edegem, Antwerp, Belgium

Universitair Ziekenhuis Brussel

Brussels, Belgium

University of Calgary

Calgary, Alberta, Canada

Alberta Health Services

Edmonton, Alberta, Canada

Children's & Women's Health Centre of British Columbia

Vancouver, British Columbia, Canada

The University of British Columbia

Vancouver, British Columbia, Canada

Hamilton General Hospital

Hamilton, Ontario, Canada

London Health Sciences Centre - University Hospital

London, Ontario, Canada

Ottawa Heart Institute

Ottawa, Ontario, Canada

Toronto General Hospital

Toronto, Ontario, Canada

Montréal Heart Institute

Montreal, Quebec, Canada

Institut Universitaire de Cardiologie et de Pneumologie de Québec-Université Laval

Québec, Quebec, Canada

Aarhus University Hospital

Aarhus, Denmark

CHU de Bordeaux

Bordeaux, New Aquitaine, France

Shaare Zedek Medical Center

Jerusalem, Israel

Oxford University Hospitals

Oxford, Oxfordshire, United Kingdom

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NCT06188689