RecruitingPhase 3NCT06247085

A Study to Investigate Efficacy and Safety of Pegtibatinase Compared With Placebo in Participants ≥12 to ≤65 Years of Age With Classical Homocystinuria (HCU) Due to Cystathionine Beta Synthase Deficiency Receiving Standard of Care Treatment

A Phase 3, Parallel-Group Treatment, Blinded, Randomized, Placebo-Controlled Study To Assess The Efficacy And Safety Of Pegtibatinase Administered Subcutaneously In Addition To Standard Of Care In Participants With Classical Homocystinuria Due To Cystathionine Beta Synthase Deficiency (HARMONY)


Sponsor

Travere Therapeutics, Inc.

Enrollment

70 participants

Start Date

Dec 28, 2023

Study Type

INTERVENTIONAL

Conditions

Summary

The purpose of this study is to measure efficacy and safety of pegtibatinase treatment compared with placebo in participants with classical HCU receiving standard of care. Study details include: * Total Study duration: up to 38 weeks * Screening: * Initial Screening duration: up to 4 weeks * Pre-treatment Diet Standardization Period duration: up to 6 weeks * Blinded Treatment Duration: 24 weeks * 2-week blinded dose titration period * 22-week blinded assessment period * Safety Follow-Up: 4 weeks after last dose (as applicable for those not enrolling in the long term extension study, ENSEMBLE)


Eligibility

Min Age: 12 YearsMax Age: 65 Years

Plain Language Summary

Simplified for easier understanding

This clinical trial is studying a drug called Pegtibatinase and Placebo for people with homocystinuria. The study is currently recruiting participants at 52 locations.

This summary was AI-generated to explain the trial in plain language. It is not medical advice. Always discuss eligibility with your doctor before enrolling in a clinical trial.

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Interventions

DRUGPegtibatinase

Pegtibatinase BIW

OTHERPlacebo

volume-matched saline SC BIW


Locations(52)

Phoenix Children's Hospital

Phoenix, Arizona, United States

Yale University School of Medicine

New Haven, Connecticut, United States

Emory University

Atlanta, Georgia, United States

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, United States

Maine Health - Maine Medical Center

Portland, Maine, United States

Uncommon Cures

Chevy Chase, Maryland, United States

The Mount Sinai Hospital

New York, New York, United States

Science 37 - Virtual Site

Morrisville, North Carolina, United States

Oregon Health and Science University

Portland, Oregon, United States

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

University of Pittsburgh Medical Center - Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, United States

University of Texas Southwestern Medical Center

Dallas, Texas, United States

Utah Health - The University of Utah Primary Children's Hospital

Salt Lake City, Utah, United States

Royal Adelaide Hospital

Adelaide, Australia

Royal Children's Hospital Melbourne

Parkville, Australia

Westmead Hospital

Westmead, Australia

Cliniques Universitaires Saint-Luc

Brussels, Belgium

Universitair Ziekenhuis Antwerpen (UZA)

Edegem, Belgium

Assistance Publique - Hôpitaux de Paris (AP-HP) - Hôpital Necker-Enfants Malades

Paris, France

CHRU Hôpitaux de Tours - Hôpital Bretonneau

Tours, France

Centre Hospitalier Régional Universitaire de Nancy (CHRU) - Hopitaux de Brabois - Hôpital d'enfants

Vandœuvre-lès-Nancy, France

Universitätsklinikum Hamburg-Eppendorf

Hamburg, Germany

Universitätsklinikum Leipzig

Leipzig, Germany

Universitätsklinikum Münster

Münster, Germany

Children's Health Ireland (CHI) at Temple Street

Dublin, Ireland

Ospedale Pediatrico Giovanni XXIII

Bari, Italy

IRCCS Istituto Giannina Gaslini

Genova, Italy

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico (Policlinico di Milano)

Milan, Italy

Fondazione IRCCS San Gerardo Dei Tintori - Ospedale San Gerardo

Monza, Italy

Azienda Ospedaliera di Padova

Padova, Italy

SP ZOZ Szpital Uniwersytecki w Krakowie

Krakow, Poland

Instytut Matki i Dziecka

Warsaw, Poland

Instytut Pomnik-Centrum Zdrowia Dziecka

Warsaw, Poland

Unidade Local de Saúde de Coimbra, EPE - Hospitais da Universidade de Coimbra

Coimbra, Portugal

Unidade Local de Saúde de Santa Maria, EPE - Hospital de Santa Maria

Lisbon, Portugal

Unidade Local de Saúde de São João, EPE - Hospital São João

Porto, Portugal

Hamad General Hospital

Doha, Qatar

Sidra Hospital

Doha, Qatar

King Abdullah International Medical Research Center

Riyadh, Saudi Arabia

King Faisal Specialist Hospital and Research Centre (KFSHRC) - Riyadh

Riyadh, Saudi Arabia

Hospital Sant Joan de Déu

Barcelona, Spain

Hospital Universitario 12 de Octubre

Madrid, Spain

Hospital Universitario Ramón y Cajal

Madrid, Spain

Complejo Hospitalario Universitario de Santiago (CHUS) - Hospital Clínico Universitario

Santiago de Compostela, Spain

Hospital Universitario Virgen del Rocío

Seville, Spain

Gazi University Hospital

Ankara, Turkey (Türkiye)

Ege Üniversitesi Hastanesi Bornova

Bornova, Turkey (Türkiye)

Istanbul University Cerrahpasa Hospital

Istanbul, Turkey (Türkiye)

Birmingham Women's and Children's NHS Foundation Trust

Birmingham, United Kingdom

University Hospitals Birmingham NHS Foundation Trust - Queen Elizabeth Hospital Birmingham

Birmingham, United Kingdom

University College London Hospitals NHS Foundation Trust - National Hospital for Neurology and Neurosurgery

London, United Kingdom

Salford Royal NHS Foundation Trust - Salford Royal Hospital

Salford, United Kingdom

View Full Details on ClinicalTrials.gov

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NCT06247085


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