RecruitingPhase 2NCT06393712

A Phase 2 Trial of ALN-APP in Patients With Cerebral Amyloid Angiopathy

A Phase 2, Randomized, Double-blind, Placebo-controlled Study to Evaluate the Efficacy, Safety, Tolerability, and Pharmacodynamics of Intrathecally Administered ALN-APP in Patients With Cerebral Amyloid Angiopathy (CAA)


Sponsor

Alnylam Pharmaceuticals

Enrollment

200 participants

Start Date

May 17, 2024

Study Type

INTERVENTIONAL

Conditions

Summary

The purpose of the study is to evaluate the effect of ALN-APP on measures of CAA disease progression and to characterize the safety, tolerability, and pharmacodynamics (PD) of ALN-APP in adult patients with sporadic CAA (sCAA) and Dutch-type CAA (D-CAA). The study will be conducted over 2 periods: a 24-month double-blind treatment period and an optional 18-month open-label extension (OLE) period. The estimated duration of study participation, inclusive of screening, treatment, and additional safety follow-up, is up to 50 months.


Eligibility

Min Age: 30 Years

Inclusion Criteria4

  • Is 50 years or older
  • Has probable CAA per the Boston Criteria Version 2.0
  • Is 30 years or older
  • Has known E693Q amyloid precursor protein (APP) gene mutation for Dutch-type CAA

Exclusion Criteria6

  • Moderate or severe stage Alzheimer's disease (AD) or significant cognitive impairment (CI)
  • Has a history of previous clinical intracerebral hemorrhage (ICH) with onset less than 90 days prior to anticipated randomization in the study
  • Has alanine aminotransferase (ALT) or aspartate aminotransferase (AST) \>3×upper limit of normal (ULN) at Screening
  • Has estimated glomerular filtration rate (eGFR) \<30 mL/min/1.73m\^2 at Screening
  • Has recently received an investigational agent
  • Has had treatment with amyloid-targeting antibody

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Interventions

DRUGPlacebo

Placebo will be administered intrathecally

DRUGALN-APP

ALN-APP will be administered intrathecally


Locations(57)

Clinical Trial Site

Los Angeles, California, United States

Clinical Trial Site

Orange, California, United States

Clinical Trial Site

Palo Alto, California, United States

Clinical Trial Site

Sacramento, California, United States

Clinical Trial Site

San Francisco, California, United States

Clinical Trial Site

Aurora, Colorado, United States

Clinical Trial Site

New Haven, Connecticut, United States

Clinical Trial Site

Gainesville, Florida, United States

Clinical Trial Site

Jacksonville, Florida, United States

Clinical Trial Site

Maitland, Florida, United States

Clinical Trial Site

Naples, Florida, United States

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Chicago, Illinois, United States

Clinical Trial Site

Lexington, Kentucky, United States

Clinical Trial Site

New Orleans, Louisiana, United States

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Boston, Massachusetts, United States

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Plymouth, Massachusetts, United States

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Rochester, Minnesota, United States

Clinical Trial Site

St Louis, Missouri, United States

Clinical Trial Site

Hackensack, New Jersey, United States

Clinical Trial Site

New York, New York, United States

Clinical Trial Site

New York, New York, United States

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New York, New York, United States

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New York, New York, United States

Clinical Trial Site

Durham, North Carolina, United States

Clinical Trial Site

Canton, Ohio, United States

Clinical Trial Site

Cleveland, Ohio, United States

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Abington, Pennsylvania, United States

Clinical Trial Site

Philadelphia, Pennsylvania, United States

Clinical Trial Site

Pittsburgh, Pennsylvania, United States

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Dallas, Texas, United States

Clinical Trial Site

Dallas, Texas, United States

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Houston, Texas, United States

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San Antonio, Texas, United States

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Seattle, Washington, United States

Clinical Trial Site

Adelaide, Australia

Clinical Trial Site

Brisbane, Australia

Clinical Trial Site

Heidelberg, Australia

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Nedlands, Australia

Clinical Trial Site

Parkville, Australia

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Calgary, Canada

Clinical Trial Site

Hamilton, Canada

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Kelowna, Canada

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Moncton, Canada

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Montreal, Canada

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Montreal, Canada

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Ottawa, Canada

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Toronto, Canada

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Victoria, Canada

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Amsterdam, Netherlands

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Leiden, Netherlands

Clinical Trial Site

Nijmegen, Netherlands

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Bern, Switzerland

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Geneva, Switzerland

Clinical Trial Site

Sankt Gallen, Switzerland

Clinical Trial Site

Glasgow, United Kingdom

Clinical Trial Site

London, United Kingdom

Clinical Trial Site

London, United Kingdom

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NCT06393712


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