RecruitingPhase 3NCT06465953

Ivosidenib (IVO) Monotherapy and Azacitidine (AZA) Monotherapy in Patients With Hypomethylating Agent (HMA) Naive Myelodysplastic Syndromes (MDS) With an IDH1 Mutation

A Phase 3, Multicenter, Open Label, Randomized, Non-comparative Two-arm Study of Ivosidenib (IVO) Monotherapy and Azacitidine (AZA) Monotherapy in Adult Patients With Hypomethylating Agent (HMA) Naive Myelodysplastic Syndromes (MDS) With an Isocitrate Dehydrogenase-1 (IDH1) Mutation (PyramIDH Study)


Sponsor

Institut de Recherches Internationales Servier

Enrollment

48 participants

Start Date

Dec 3, 2024

Study Type

INTERVENTIONAL

Conditions

Summary

This study will enroll participants with myelodysplastic syndromes (MDS) with an Isocitrate dehydrogenase protein, 1 (IDH1) mutation, who have not received treatment with a hypomethylating agent previously. Participants will be randomized to receive either ivosidenib (IVO) alone or azacitidine (AZA) alone. IVO will be administered daily throughout the 28-day treatment cycle and AZA will be administered for the first 7 days of each 28-day cycle. Study visits will be conducted every week during Cycle 1 (Days 1, 8, 15, and 22), and Day 1 of each cycle thereafter. After the last dose of treatment, participants will attend an safety follow-up visit and participants will be followed to assess overall survival. Study visits may include a bone marrow aspirate, physical exam, echocardiogram (ECHO), electrocardiogram (ECG), blood and urine analysis, and questionnaires.


Eligibility

Min Age: 18 Years

Inclusion Criteria7

  • Diagnosis of HMA naive IDH1 R132 mutated MDS defined according to WHO criteria (5th edition):
  • Moderate high, high and very high-risk MDS per IPSS-M score will be eligible regardless of blood counts and with blast counts 0-19%.
  • Low and moderate low-risk MDS per IPSS-M score must:
  • Have cytopenias related to MDS, defined as: <100 platelets/microliter, or absolute neutrophil count (ANC) <1000/mm3, or hemoglobin <10g/dL AND
  • Have a blast count between 5-19% AND
  • Be eligible for HMA therapy (very low risk participants are to be excluded)
  • Locally or centrally confirmed IDH1 R132 C/G/H/L/S mutation

Exclusion Criteria2

  • Received prior anticancer/disease modifying treatment for MDS (including HMA's, cytotoxic chemotherapy, investigational agents, bcl-2 inhibitor based-regimens, hematopoietic stem cell transplant (HSCT), IDH1 inhibitors). For LR-MDS patients, prior treatment with growth factors, luspatercept, lenalidomide, and imetelstat are allowed.
  • >20% blasts by morphology or immunohistochemistry on screening bone marrow aspirate/biopsy

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Interventions

DRUGIvosidenib

Two 250 mg tablets, totaling 500 mg, administered orally once daily until disease relapse or progression, unacceptable toxicity, confirmed pregnancy, undergoing HSCT, death, withdrawal of consent, lost to follow-up, or Sponsor ending the study, whichever occurs first.

DRUGAzacitidine

Azacitidine 75mg/m\^2/day administered by subcutaneous (SC) or intravenous (IV) injection for 1 week (7 days) of each 4-week (28 day) treatment cycle until disease relapse or progression, unacceptable toxicity, confirmed pregnancy, undergoing HSCT, death, withdrawal of consent, lost to follow-up, or Sponsor ending the study, whichever occurs first.


Locations(62)

Presbyterian / St. Luke'S Medical Center

Denver, Colorado, United States

University of Chicago, Duchossois Center for Advanced Medicine (DCAM)

Chicago, Illinois, United States

Massachusetts General Hospital

Boston, Massachusetts, United States

MSKCC

New York, New York, United States

Unc Lineberger Comprehensive Cancer Center

Chapel Hill, North Carolina, United States

Ohio State University Comprehensive Cancer Center

Columbus, Ohio, United States

Oncology Associates of Oregon

Eugene, Oregon, United States

University of Texas UT Southwestern Comprehensive Cancer Center

Dallas, Texas, United States

MD Anderson Cancer Centre

Houston, Texas, United States

Royal Adelaide Hospital

Adelaide, Australia

Monash Health

Clayton, Australia

Northern Health

Epping, Australia

Liverpool Hospital

Liverpool, Australia

Sir Charles Gairdner Hospital

Nedlands, Australia

Calvary Mater Newcastle

Waratah, Australia

Liga Paranaense de Combate ao Câncer - Hospital Erasto Gaertner

Curitiba, Brazil

Centro de Pesquisa Clínica - Hospital Nove de Julho

São Paulo, Brazil

Real E Benemérita Associação Portuguesa de São Paulo

São Paulo, Brazil

Hospital das Clínicas da Faculdade de Medicina da USP

São Paulo, Brazil

Sociedade Beneficente Israelita Brasileira Hospital Albert Einstein

São Paulo, Brazil

Casa de Saúde Santa Marcelina

São Paulo, Brazil

Centro de Pesquisas Clínicas da Fundação Doutor Amaral Carvalho

São Paulo, Brazil

Instituto Nacional do Câncer

São Paulo, Brazil

Chu Nantes-Hotel Dieu

Nantes, France

Chu de Nice - Hôpital L'Archet 1

Nice, France

Hopital Saint Louis

Paris, France

Chu Bordeaux, Hopital Du Haut Leveque

Pessac, France

Institut Universitaire Du Cancer Toulouse-Oncopole

Toulouse, France

Chu Brabois

Vandœuvre-lès-Nancy, France

Universitatsklinikum Dresden Carl Gustav Carus

Dresden, Germany

Marien Hospital Duesseldorf

Düsseldorf, Germany

Universitaetsmedizin Goettingen (Umg)

Göttingen, Germany

Universitaetsklinikum Leipzig

Leipzig, Germany

Tum Klinikum Rechts Der Isar

Munich, Germany

Azienda Ospedaliero Universitaria Delle Marche

Ancona, Italy

Istituto Di Ematologia "Lorenzo E Ariosto Seragnoli" - Policlinico Di S. Orsola

Bologna, Italy

Azienda Ospedaliero-Universitaria Careggi

Florence, Italy

Humanitas Research Hospital (Istituto Clinico Humanitas)

Milan, Italy

Fondazione I.R.C.C.S. Policlinico San Matteo

Pavia, Italy

Dipartimento Di Biomedicina E Prevenzione - Universita Degli Studi Di Roma "Tor Vergata"

Roma, Italy

Azienda Ospedaliera Universitaria Citta Della Salute E Della Scienza Di Torino - Presidio Molinette

Torino, Italy

University of Fukui Hospital

Yoshida-gun, Eiheiji-cho 670-8540 Himeji, Japan

Kyushu University Hospital

Higashi-ku, Fukuoka-city, Fukuoka, Japan

Japanese Red Cross Society Himeji Hospital

Himeji-city, Hyogo, Japan

Tokai University Hospital

Isehara-city, Kanagawa, Japan

Japanese Red Cross Musashino Hospital

Musashino-city, Tokyo, Japan

Kitasato University Hospital

Sagamihara, Japan

Umc Amsterdam - Vumc

Amsterdam, Netherlands

Umc Groningen

Groningen, Netherlands

Institut Catala D' Oncologia

Badalona, Spain

H. Valle de Hebron

Barcelona, Spain

Clinica Universitaria de Navarra (Madrid)

Madrid, Spain

Clinica Universitaria de Navarra (Pamplona)

Pamplona, Spain

Hospital Clinico Universitario de Salamanca

Salamanca, Spain

Hospital Universitario Virgen de La Macarena

Seville, Spain

H. Universitario La Fe

Valencia, Spain

Western General Hospital

Edinburgh, United Kingdom

St James' University Hospital

Leeds, United Kingdom

University College London Hospital

London, United Kingdom

Kings College Hospital

London, United Kingdom

Churchill Hospital

Oxford, United Kingdom

Torbay Hospital

Torquay, United Kingdom

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