RecruitingNCT06472557

Spinocerebellar Ataxia Type 27B Natural History Study (SCA27B-NHS)


Sponsor

University Hospital Tuebingen

Enrollment

300 participants

Start Date

Jun 4, 2024

Study Type

OBSERVATIONAL

Conditions

Summary

This international, multi-center, multi-modal, and prospective observational cohort study aims to validate trial outcomes for capturing disease progression in Spinocerebellar Ataxia Type 27B (SCA27B), with combined multi-modal capture of clinical outcome assessments, digital-motor assessments, and molecular biomarkers.


Eligibility

Min Age: 18 YearsMax Age: 99 Years

Inclusion Criteria5

  • SCA27B: genetic diagnosis of ≥250 uninterrupted GAA repeat expansions in FGF14
  • SCA27B risk subject: asymptomatic first-degree relative of SCA27B participant with known or unknown carrier status
  • Unrelated healthy controls: no signs or history of neurological or psychiatric disease AND
  • Written informed consent AND
  • Participants are willing and able to comply with study procedures

Exclusion Criteria3

  • SCA27B: Missing informed consent
  • SCA27B risk subjects: Missing informed consent
  • Unrelated healthy controls: Missing informed consent, or concurrent neurological, orthopedic, or other diseases interfering with the motor assessments

Interested in this trial?

Get notified about updates and connect with the research team.


Locations(5)

Department of Neurology, Motol University Hospital, Second Faculty of Medicine, Charles University

Prague, Czechia

Center for Neurology & Hertie-Institute for Clinical Brain Research, Dept. for Neurodegenerative Diseases

Tübingen, Baden-Wurttemberg, Germany

Department of Neurology & Center for Translational Neuro- and Behavioral Sciences, Essen University Hospital, University of Duisburg-Essen

Essen, North Rhine-Westphalia, Germany

IRCCS Fondazione Stella Maris

Pisa, Italy

Department of Neurology, Donostia University Hospital, BioGipuzkoa Health Research Institute

San Sebastián, Gipuzkoa, Spain

View Full Details on ClinicalTrials.gov

For the most up-to-date information, visit the official listing.

Visit

NCT06472557