RecruitingPhase 3NCT06597019

Study to Evaluate Efficacy and Safety of Inclisiran in Children With Heterozygous Familial Hypercholesterolemia

Two Part (Double-blind Inclisiran Versus Placebo [Year 1] Followed by Open-label Inclisiran [Year 2]) Randomized Multicenter Study to Evaluate Safety, Tolerability and Efficacy of Inclisiran in Children (6 to Less Than 12 Years) With Heterozygous Familial Hypercholesterolemia and Elevated LDL- Cholesterol


Sponsor

Novartis Pharmaceuticals

Enrollment

51 participants

Start Date

Dec 9, 2024

Study Type

INTERVENTIONAL

Conditions

Summary

This is a pivotal phase III study designed to evaluate safety, tolerability, and efficacy of inclisiran in children (aged 6 to \<12 years) with heterozygous familial hypercholesterolemia (HeFH) and elevated low density lipoprotein cholesterol (LDLC).


Eligibility

Min Age: 6 YearsMax Age: 11 Years

Inclusion Criteria5

  • Male or female participants, 6 to \<12 years of age at screening
  • HeFH diagnosed either by genetic testing or on phenotypic criteria
  • Fasting LDL-C \>130 mg/dL (3.4 mmol/L) at screening
  • For participants 8 to \<12 years, on an optimal dose of statin (investigator's discretion) unless statin intolerant, with or without other lipid-lowering therapy (e.g. ezetimibe). For participants \<8 years, the use of background lipid-lowering treatment is based on investigator's discretion.
  • Participants on lipid-lowering therapies (such as statin and/or e.g. ezetimibe) must be on a stable dose for ≥30 days before screening with no planned medication or dose changes during study participation.

Exclusion Criteria7

  • Previous treatment (within 90 days of screening) with monoclonal antibodies directed towards PCSK9
  • Secondary hypercholesterolemia, e.g. hypothyroidism or nephrotic syndrome
  • Homozygous familial hypercholesterolemia (HoFH)
  • Body weight \<16 kg at the screening and/or randomization (Day 1) visit
  • Active liver disease defined as any known current infectious, neoplastic, or metabolic pathology of the liver or unexplained alanine aminotransferase (ALT), aspartate aminotransferase (AST) elevation \>3x ULN, or total bilirubin elevation \>2x ULN (except patients with Gilbert's syndrome)
  • Pregnant or nursing females
  • Recent and/or planned use of other investigational medicinal products or devices

Interventions

DRUGInclisiran

Inclisiran (inclisiran sodium 300 mg subcutaneous (s.c.) for participants with body weight ≥23 kg and inclisiran sodium 180 mg s.c. for participants with body weight \<23 kg. The dose level is based on the participant's body weight on Day 1 (for Part 1) and Day 360 (for Part 2), respectively.

DRUGPlacebo

Sterile normal saline (0.9% sodium chloride in water for subcutaneous injection)


Locations(66)

UC San Francisco Medical Center

San Francisco, California, United States

UC San Francisco Medical Center

San Francisco, California, United States

Children's National Hospital

Washington D.C., District of Columbia, United States

Childrens National Hospital

Washington D.C., District of Columbia, United States

Excel Medical Clinical Trials LLC

Boca Raton, Florida, United States

Icahn School of Med at Mt Sinai

New York, New York, United States

Primary Childrens Medical Center

Salt Lake City, Utah, United States

Primary Childrens Medical Center

Salt Lake City, Utah, United States

Virginia Commonwealth University

Richmond, Virginia, United States

West Virginia Childrens Hospital

Morgantown, West Virginia, United States

West Virginia Childrens Hospital

Morgantown, West Virginia, United States

Novartis Investigative Site

Buenos Aires, Argentina

Novartis Investigative Site

CABA, Argentina

Novartis Investigative Site

Salzburg, Austria

Novartis Investigative Site

Vienna, Austria

Novartis Investigative Site

Brussels, Belgium

Novartis Investigative Site

Leuven, Belgium

Novartis Investigative Site

Fortaleza, Ceará, Brazil

Novartis Investigative Site

Rio de Janeiro, Rio de Janeiro, Brazil

Novartis Investigative Site

Porto Alegre, Rio Grande do Sul, Brazil

Novartis Investigative Site

São Paulo, São Paulo, Brazil

Novartis Investigative Site

Beijing, Beijing Municipality, China

Novartis Investigative Site

Shanghai, China

Novartis Investigative Site

Prague, Czechia

Novartis Investigative Site

Prague, Czechia

Novartis Investigative Site

Marseille, France

Novartis Investigative Site

Nantes, France

Novartis Investigative Site

Paris, France

Novartis Investigative Site

Freiburg im Breisgau, Baden-Wurttemberg, Germany

Novartis Investigative Site

Frankfurt am Main, Hesse, Germany

Novartis Investigative Site

Hanover, Germany

Novartis Investigative Site

Athens, Greece

Novartis Investigative Site

Ioannina, Greece

Novartis Investigative Site

Hong Kong, Hong Kong

Novartis Investigative Site

Budapest, Hungary

Novartis Investigative Site

Jerusalem, Israel

Novartis Investigative Site

Ramat Gan, Israel

Novartis Investigative Site

Milan, MI, Italy

Novartis Investigative Site

Roma, RM, Italy

Novartis Investigative Site

Torino, TO, Italy

Novartis Investigative Site

Verona, VR, Italy

Novartis Investigative Site

Kuala Lumpur, Kuala Lumpur, Malaysia

Novartis Investigative Site

Amsterdam, North Holland, Netherlands

Novartis Investigative Site

Bialystok, Poland

Novartis Investigative Site

Gdansk, Poland

Novartis Investigative Site

Lodz, Łódź Voivodeship, Poland

Novartis Investigative Site

Coimbra, Portugal

Novartis Investigative Site

Lisbon, Portugal

Novartis Investigative Site

Porto, Portugal

Novartis Investigative Site

Porto, Portugal

Novartis Investigative Site

Bloemfontein, Free State, South Africa

Novartis Investigative Site

Elche, Alicante, Spain

Novartis Investigative Site

Cadiz, Andalusia, Spain

Novartis Investigative Site

Esplugues, Barcelona, Spain

Novartis Investigative Site

Badalona, Catalonia, Spain

Novartis Investigative Site

Pamplona, Navarre, Spain

Novartis Investigative Site

Barcelona, Spain

Novartis Investigative Site

Málaga, Spain

Novartis Investigative Site

Seville, Spain

Novartis Investigative Site

Taipei, Taiwan

Novartis Investigative Site

Taipei, Taiwan

Novartis Investigative Site

Adana, Saricam, Turkey (Türkiye)

Novartis Investigative Site

Ankara, Yenimahalle, Turkey (Türkiye)

Novartis Investigative Site

Izmir, Turkey (Türkiye)

Novartis Investigative Site

West Midlands, Birmingham, United Kingdom

Novartis Investigative Site

London, United Kingdom

View Full Details on ClinicalTrials.gov

For the most up-to-date information, visit the official listing.

Visit

NCT06597019