RecruitingPhase 3NCT06672237

A Phase 3 Study of NTLA-2001 in ATTRv-PN

MAGNITUDE-2: A Phase 3, Multinational, Randomized, Double-Blind, Placebo-Controlled Study to Evaluate the Efficacy and Safety of NTLA-2001 in Participants With Hereditary Transthyretin Amyloidosis With Polyneuropathy (ATTRv-PN)


Sponsor

Intellia Therapeutics

Enrollment

60 participants

Start Date

Nov 22, 2024

Study Type

INTERVENTIONAL

Summary

This study will be conducted to evaluate the efficacy and safety of a single dose of nexiguran ziclumeran (NTLA-2001) compared to placebo in participants with ATTRv-PN.


Eligibility

Min Age: 18 YearsMax Age: 85 Years

Inclusion Criteria2

  • Diagnosis of ATTRv-PN
  • Karnofsky Performance Status (KPS) ≥ 60

Exclusion Criteria10

  • Other causes of amyloidosis (amyloidosis caused by non-TTR protein)
  • Other known causes of sensorimotor or autonomic neuropathy
  • Diabetes mellitus
  • New York Heart Association Class III or IV heart failure
  • Liver failure
  • Hepatitis B, hepatitis C or human immunodeficiency virus (HIV) infection
  • Prior receipt of a TTR silencer (Small interfering RNA (siRNA) or Antisense oligonucleotides (ASOs))
  • Estimated Glomerular Filtration Rate < 30 mL/min/1.73 m2
  • Unable or unwilling to take vitamin A supplementation for the duration of the study
  • History of liver disease

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Interventions

BIOLOGICALnexiguran ziclumeran

nexiguran ziclumeran 55 mg by single IV infusion

DRUGNormal Saline as Placebo

Normal saline (0.9% NaCl) by single IV infusion


Locations(14)

Hospital Británico de Buenos Aires

Buenos Aires, Argentina

Hospital Italiano de Buenos Aires (HIBA)

Buenos Aires, Argentina

Hospital El Cruce

San Juan Bautista, Argentina

Hospital das Clinicas da Universidade Estadual de Campinas (UNICAMP)

Campinas, Brazil

HCFMRP - Hospital das Clinicas da Faculdade de Medicina de Ribeirao Preto

Ribeirão Preto, Brazil

Instituto de Educacao, Pesquisa e Gestao em Saude

Rio de Janeiro, Brazil

PSEG Centro de Pesquisa Clinica S.A.

São Paulo, Brazil

National Institute of Medical Sciences and Nutrition - Salvador Zubiran (INCMNSZ)

Tlalpan, Mexico

National University Hospital

Singapore, Singapore

Singapore General Hospital

Singapore, Singapore

National Taiwan University Hospital

Taipei, Taiwan

Taipei Veterans General Hospital

Taipei, Taiwan

Chang Gung Medical Foundation - Linkou Branch

Taoyuan, Taiwan

Siriraj Hospital

Bangkok, Thailand

View Full Details on ClinicalTrials.gov

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NCT06672237