RecruitingPhase 2NCT07169279

Interventional Study of Infigratinib in Children < 3 Years Old With Achondroplasia (ACH)

Phase 2b, Randomized, Double-Blind, Placebo-Controlled Clinical Trial, Preceded by a Single Ascending Dose Portion and a Phase 2 Open-Label Portion, to Evaluate the Safety and Efficacy of Oral Infigratinib in Infants and Young Children With Achondroplasia


Sponsor

QED Therapeutics, a BridgeBio company

Enrollment

77 participants

Start Date

Nov 19, 2025

Study Type

INTERVENTIONAL

Conditions

Summary

This is a Phase 2, multicenter, randomized, placebo-controlled study to evaluate the safety and efficacy of infigratinib in participants \< 3 years old with ACH. The purposes of the SAD and Phase 2 portions are to identify and confirm the dose of infigratinib to be used in the Phase 2b portion, based on safety and PK. The purpose of the Phase 2b, placebo-controlled portion is to evaluate the safety and efficacy of infigratinib in children \< 3 years old with ACH at the selected dose.


Eligibility

Min Age: 0 YearsMax Age: 32 Months

Inclusion Criteria7

  • Diagnosis of ACH confirmed by genetic testing. If prospective participants had prior genetic testing, the diagnosis must be confirmed by a report from a certified laboratory, documenting the specific mutation.
  • Age 0 to 32 months (2 years and 8 months) at screening.
  • Signed informed consent, which must be obtained from each participant's parent(s) or legal guardian.
  • Parent(s)/Guardian(s) willing and able to attend all study visits and comply with all study requirements.
  • Parent(s)/Guardian(s) willing and able to comply with the routine care of the study participants according to local guidance for the management of infants and young children with ACH.
  • Able to swallow age-appropriate oral medication.
  • In participants <1 year old, be compliant with recommended vitamin D supplementation of 5 10 μg/day or higher (or as recommended by country specific guidelines).

Exclusion Criteria10

  • Participants who have hypochondroplasia or diagnosis of genetic condition other than ACH, or any clinical condition that can affect growth.
  • Gestational age at birth <37 weeks and/or birth weight <2500 grams.
  • Gastroesophageal reflux disease requiring prolonged treatment (>1 week) with prohibited medications.
  • Evidence of cervicomedullary compression, as defined by an Achondroplasia Foramen Magnum Score (AFMS) 4, symptomatic or asymptomatic, diagnosed during MRI done at screening or a previous MRI done at any time if the participant had not undergone decompression surgery.
  • History of fracture of a long bone or spine within 6 months prior to screening.
  • Any other significant concurrent disease or condition that, in the view of the investigator and/or sponsor, would confound assessment of efficacy or safety of infigratinib and/or would require treatment with a prohibited medication (per protocol), and/or would place the participant at high risk for poor treatment compliance or for failure to complete the study.
  • Having received or planning to receive treatment with any other investigational or approved product for the treatment of ACH or short stature, including (but not limited to) r-hGH, IGF-1, CNP analog, FGF ligand trap, or treatment targeting FGFR inhibition at any time.
  • Regular long-term (>3 weeks; more than twice/year) treatment with supraphysiologic doses of glucocorticoid therapy (ie, >15 mg/m2/day of hydrocortisone or equivalent) or treatment with glucocorticoids at anti-inflammatory doses (for over 3 weeks within 6 months of the screening visit. NOTE: Low-dose topical, inhaled, or intranasal corticosteroids are acceptable.
  • Significant abnormality in screening laboratory results,
  • Allergy or hypersensitivity to any components of the study drug.

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Interventions

DRUGInfigratinib is provided as a single dose of minitablets for oral administration

* The initial cohort dose of infigratinib will begin at the protocol-specified starting dose, with subsequent cohort escalation based on protocol specific criteria. * The target dose is the dose that will provide similar exposure to the dose of 0.25 mg/kg/day in participants 3 years old and older. * The dose and number of minitablets will be calculated based on individual participant age and weight.

DRUGInfigratinib is provided as sprinkle capsules for daily oral administration

* The cohort dose of infigratinib will be the dose identified in the Single Ascending Dose portion for the age group. * The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months.

DRUGInfigratinib or placebo comparator is provided as sprinkle capsules for daily oral administration

* The cohort dose of infigratinib or placebo will be the dose confirmed in the Phase 2 portion for the age group. * The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months.

DRUGInfigratinib is provided as sprinkle capsules for daily oral administration

* The dose of infigratinib will be the dose confirmed in the Phase 2 portion and used in the Phase 2b portion for the age group. * The dose and number of sprinkle capsules/day will be calculated based on individual participant age and weight. Doses will be adjusted based on age and weight changes approximately every 3 months for the first year and every 6 months thereafter.


Locations(13)

UCSF Benioff Children's Hospital

Oakland, California, United States

Johns Hopkins University

Baltimore, Maryland, United States

University of Wisconsin Madison - Waisman Center Bone Dysplasia Clinic

Madison, Wisconsin, United States

Murdoch Children's Research Institute

Parkville, Victoria, Australia

Children's Hospital of Eastern Ontario Research Institute

Ottawa, Ontario, Canada

Université de Montréal - Centre Hospitalier Universitaire Sainte-Justine

Montreal, Quebec, Canada

Paediatric Clinical Research Unit at Oslo University Hospital

Oslo, Norway

KK Women's and Children's Hospital

Singapore, Singapore

Unidad de Cirugia Artroscopica (UCA)

Vitoria-Gasteiz, Spain

NHS Greater Glasgow and Clyde

Glasgow, United Kingdom

Guy's and Saint Thomas' NHS Foundation Trust

London, United Kingdom

Manchester University NHS Foundation Trust

Manchester, United Kingdom

Sheffield Children's NHS Foundation Trust

Sheffield, United Kingdom

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NCT07169279


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