RecruitingNCT04176523

Understanding the Long-Term Management of Organic Acidemia Patients With CARBAGLU®: A Mixed Methods Approach


Sponsor

RECORDATI GROUP

Enrollment

95 participants

Start Date

Jan 15, 2019

Study Type

OBSERVATIONAL

Conditions

Summary

This is a prospective mixed-design study focused on the long-term management of propionic aciduria (PA) and methylmalonic aciduria (MMA) with N-carbamylglutamate (NCG) maintenance therapy. Treatment characteristics, clinical outcomes, and healthcare utilization data of patients diagnosed PA or MMA treated \>6 months therapy with NCG are collected at baseline, 12 months, 18 months, 36 months and 54 months. Qualitative interviews with adult patients and caregivers are conducted \>6 months after study enrollment to gain a better understanding of the disease burden and the treatment burden of patients and their families.


Eligibility

Min Age: 6 MonthsMax Age: 99 Years

Inclusion Criteria5

  • Patient has confirmed diagnosis of an organic acidemia (e.g., MMA or PA)
  • Patient initiated treatment with carglumic acid for long-term management of MMA or PA
  • Patient has been treated with carglumic acid for a minimum of 6 months
  • Patient (or caregiver) is able to comply with all prospective study procedures
  • Patient (or caregiver) is able to provide informed consent

Exclusion Criteria1

  • None

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Interventions

DRUGCarglumic Acid

Maintenance therapy with carglumic acid


Locations(32)

Hopital Des Enfants, CHU de Bordeaux-GH Pellegrin

Bordeaux, France

Hopital de la Conception

Marseille, France

Hôpital de la Timone

Marseille, France

CHU de Nancy - Hopitaux de Brabois

Nancy, France

Hôpital Necker Enfants Malades

Paris, France

CHU de Rouen

Rouen, France

Nouvel Hopital Civil

Strasbourg, France

Hopital de Hautepierre

Strasbourg, France

Klinikum Bremen Mitte, Prof. Hess Kinderklinik

Bremen, Germany

Azienda Ospedaliero Universitaria Meyer

Florence, Italy

San Paola Hospital, ASST Santi Paolo e Carlo

Milan, Italy

Milan Policlinico University

Milan, Italy

Azienda Ospedaliera San Gerardo Monza

Monza, Italy

Azienda Ospedaliera Universitaria Federico II

Naples, Italy

University Hospital of Padova

Padova, Italy

Turin University Hospital

Turin, Italy

Oslo University Hospital

Oslo, Norway

AMM hospital val d'hebron

Barcelona, Spain

Sant Joan de Deu

Barcelona, Spain

Universitario de Cruces

Bilbao, Spain

Hospital Infantil Universitario Nino Jesus

Madrid, Spain

Hospital 12 de Octubre

Madrid, Spain

Hospital Universitario La Paz

Madrid, Spain

Universitario Ramon y Cajal Madrid

Madrid, Spain

Hospital Universitario Virgen de la Arrixaca

Murcia, Spain

Hospital Universitario Son Espases

Palma de Mallorca, Spain

Hospital Universitario Virgen del Rocio

Seville, Spain

Universitario Miguel Servet

Zaragoza, Spain

NÄL

Trollhättan, Sweden

Guy's and St. Thomas' Hospital NHS Foundation Trust

London, United Kingdom

Great Ormond Street Hospital

London, United Kingdom

Sheffield Children's Hospital NHS Foundation Trust

Sheffield, United Kingdom

View Full Details on ClinicalTrials.gov

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NCT04176523


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