RecruitingNCT05769621

A Retrospective Study to Characterize Participants With Propionic Acidemia

A Retrospective Cohort Study to Characterize Propionic Acidemia Patients


Sponsor

ModernaTX, Inc.

Enrollment

60 participants

Start Date

Jun 16, 2023

Study Type

OBSERVATIONAL

Conditions

Summary

This is a non-interventional, observational, global, multicenter, study describing participant characteristics, clinical outcomes, and event rates in participants with propionic acidemia (PA).


Eligibility

Min Age: 2 Years

Inclusion Criteria13

  • Participants' medical records are eligible for abstraction only if all of the following criteria apply:
  • Confirmed diagnosis of PA based on diagnosis by molecular genetic testing (propionyl-CoA carboxylase subunitα\[PCCA\] and/or propionyl-CoA carboxylase subunitβ\[PCCB\] mutations).
  • Participant provided informed consent (and assent, as applicable).
  • Medical records with sufficient data to support medical encounter for CEC adjudication (MEA adjudication) must be available dating back to birth or 01 January 2015, whichever occurs later. Participants born prior to 2015 will require additional information to confirm eligibility.
  • Experienced at least one MDE in the 24 months preceding the Index Date or experienced at least 3 MDEs within any one 12-month retrospective review period (based on Index Date) dating back to birth or 01 January 2015, whichever occurs later.
  • Must have a confirmed age (months) of disease onset (early or late, where early is defined as the neonatal period).
  • Censoring Criteria:
  • Participants medical records meeting the following censoring criterion will not be abstracted:
  • Participation in a clinical study of any investigational agent.
  • Received gene therapy treatment
  • Confirmed organ transplantation
  • Investigator is no longer able to obtain relevant clinical information of the participant.
  • Death

Exclusion Criteria1

  • \- Participation (prior or ongoing) in clinical study mRNA-3927-P101 (NCT04159103) or mRNA-3927-P101-EXT (NCT05130437).

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Locations(29)

University of Stanford Medical Center

Stanford, California, United States

Johns Hopkins University

Baltimore, Maryland, United States

University of Michigan Hospital

Ann Arbor, Michigan, United States

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Texas Children's Hospital

Houston, Texas, United States

Seattle Children's Hospital

Seattle, Washington, United States

Royal Children's Hospital Melbourne

Parkville, Victoria, Australia

Stollery Children's Hospital University of Alberta

Edmonton, Alberta, Canada

CHU Toulouse

Toulouse, Haute-Garonne, France

CHRU Nancy Hôpital des Enfants

Vandœuvre-lès-Nancy, Meurthe-et-Moselle, France

Hôpital Necker - Enfants Malades

Paris, Paris, France

CHU de Marseille - Hôpital de la Timone

Marseille, France

Azienda Ospedaliera Universitaria Federico II

Naples, Campania, Italy

ASST di Monza - Azienda Ospedaliera San Gerardo

Monza, Monza A Brianza, Italy

Azienda Ospedaliero Universitaria A Meyer - INCIPIT - PIN

Florence, Tuscany, Italy

Fujita Health University Hospital

Toyoake, Aichi-ken, Japan

The Jikei University School of Medicine

Minato, Tokyo, Japan

Erasmus MC

Rotterdam, South Holland, Netherlands

Hospital Sant Joan de Deu

Esplugues de Llobregat, Barcelona, Spain

Hospital Universitario Marques de Valdecilla

Santander, Cantabria, Spain

Hospital Universitario Cruces

Barakaldo, Spain

Hospital Universitario Raymon y Cajal

Madrid, Spain

Hospital Universitario 12 de Octubre

Madrid, Spain

Hospital Universitario Virgen del Rocio - PPDS

Seville, Spain

Hospital Universitari I Politecnic La Fe de Valencia

Valencia, Spain

Victoria Hospital

Kirkcaldy, Fife, United Kingdom

St Mary's Hospital - PPDS

Manchester, Lancashire, United Kingdom

Great Ormond Street Hospital

City of London, London, United Kingdom

University Hospital Birmingham

Birmingham, United Kingdom

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NCT05769621


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