RecruitingNCT04194619

Pregnancy in Women With Rare Multisystemic Vascular Diseases: COGRare5 Study

A National Prospective Cohort for Pregnancies in Patients With Rare Vascular Anomalies: COGRare5 Study


Sponsor

Hospices Civils de Lyon

Enrollment

400 participants

Start Date

Feb 6, 2020

Study Type

OBSERVATIONAL

Conditions

Summary

There are no prospective studies of pregnancies for the diseases studied here in (Heredity Hemorrhagic Telangiectasia, Marfan syndrome or related, primary lower limb lymphedema, superficial arteriovenous malformations, and cerebro-spinal arteriovenous malformations) although complications of these can present life-threatening health problems for the mother and her baby. The purpose of this National prospective study is to obtain greater insight into obstetrical complications associated with rare maternal vascular genetic disorders in order to improve prevention and to reduce risk of death. In this context, experts and patient associations consider that there is a need to make real progress in the formulation of recommendations based on scientific data.


Eligibility

Sex: FEMALEMin Age: 18 YearsMax Age: 45 Years

Inclusion Criteria5

  • Women aged ≥ 18 years and ≤45 years at the time of inclusion
  • Pregnant and/or having given birth less than 1 month (≤ 30 days)
  • Clinically and/or radiological and/or molecular biology diagnosis of a rare vascular disease before or during pregnancy or one month after delivery.
  • Having been informed of all pertinent aspects of the study and provided oral non-opposition.
  • Major under legal protection

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Interventions

OTHERQuestionnaire

Interview of women with a rare vascular disease through a phone questionnaire about severe and specific obstetrical complications during and after pregnancy.


Locations(36)

Service de Médecine Interne et Maladies Vasculaires + Service Neuropédiatrie et neurochirurgie de l'enfant - CHU Angers

Angers, France

Service de Médecine interne et immunologie clinique + Service de Médecine Vasculaire - Hôpital Saint André, CHU de Bordeaux

Bordeaux, France

Service Pneumologie et Oncologie Thoracique - AP-HP Hôpital Ambroise Paré

Boulogne-Billancourt, France

Centre de Référence pour la maladie de Rendu-Osler - Service Génétique Clinique - Hôpital Femme-Mère-Enfant - Hospices Civils de Lyon

Bron, France

Service d'imagerie médicale - Neuroradiologie interventionnelle - Hôpital Neurologique P. Wertheimer - HCL

Bron, France

Service d'Imagerie Pédiatrique et Fœtale et Consultation Pluridisciplinaire des Angiomes - Hôpital Femme-Mère-Enfant - HCL

Bron, France

Service de Génétique, Hôpital Femme-Mère-Enfant

Bron, France

Service de Médecine Vasculaire - Hôpital de la Côte de Nacre

Caen, France

Service Médecine Interne Estaing CHU de Clermont-Ferrand - Hôpital d'Estaing

Clermont-Ferrand, France

CHU Dijon Bourgogne - Hôpital François Mitterrand

Dijon, France

Service de Médecine vasculaire et HTA - Hôpital Albert Calmette, CHRU de Lille

Lille, France

Service Médecine interne - CHRU de Lille - Hôpital Claude Huriez

Lille, France

CHU de Marseille - Hôpital de la Timone

Marseille, France

Service Médecine Interne - Hôpital Saint-Eloi, CHU de Montpellier

Montpellier, France

Service de neuroradiologie diagnostique et interventionnelle - CHU de Nancy, Hôpital St-Julien

Nancy, France

Service de Médecine Interne-Médecine Vasculaire, CHU de Nantes - Hôtel Dieu

Nantes, France

Unité de neuro-interventionnelle CHU Nice, Hôpital Pasteur 2

Nice, France

Service de dermatologie, CHU de Nice - Hôpital l'Archet 2

Nice, France

Service de Neuroradiologie - AP-HP - Paris (Hôpital Lariboisière)

Paris, France

Service de Lymphologie - Hôpital Cognacq-Jay - Paris

Paris, France

Service de Cardiologie - Hôpital Bichat, AP-HP

Paris, France

Service de Neuroradiologie Interventionnelle - Fondation Adolphe de Rothschild

Paris, France

Service Radiologie-pneumologie interventionnelle - Hôpital Tenon AP-HP

Paris, France

Service de Génétique CHU de Poitiers

Poitiers, France

Service de Pneumologie CHU de Rennes - Hôpital Pontchaillou

Rennes, France

Unité de Génétique médicale, CHU de Rennes, Hôpital Sud

Rennes, France

Service Médecine Interne - Médecine vasculaire - CHU de Rouen, Hôpital Charles Nicolle

Rouen, France

Service de Médecine Vasculaire et Thérapeutique, Explorations Fonctionnelles Vasculaires - CHU de Saint-Etienne - Hôpital Nord

Saint-Etienne, France

Clinique cardiologique et des maladies vasculaires CHU de Nantes, Hôpital G. R. LAENNEC

Saint-Herblain, France

Service Maladies vasculaires - HTA - NHC Pôle Médico-chirurgicale cardio-vasculaire, CHU de Strasbourg - Hôpital Civil

Strasbourg, France

CHU de Strasbourg, Hôpital de Hautepierre

Strasbourg, France

Service de Neuroradiologie Interventionnelle - Hôpital Foch

Suresnes, France

Service de Cardiologie _ Hôpital des Enfants (Purpan)

Toulouse, France

Service de Médecine Interne + Service Médecine Vasculaire _ Hôpital RANGUEIL

Toulouse, France

Service Pneumologie, Hôpital Bretonneau, Centre Hospitalier Régional Universitaire de TOURS

Tours, France

CHU de Nancy - Hôpitaux de Brabois

Vandœuvre-lès-Nancy, France

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NCT04194619


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