RecruitingPhase 2Phase 3NCT07010159

Phase 2/3 Study of KPL-387 in Recurrent Pericarditis

A Phase 2/3 Efficacy and Safety Study of KPL-387 Treatment in Participants With Recurrent Pericarditis


Sponsor

Kiniksa Pharmaceuticals International, plc

Enrollment

165 participants

Start Date

Jul 25, 2025

Study Type

INTERVENTIONAL

Conditions

Summary

This study is being done to demonstrate whether KPL-387 is an effective and safe treatment for recurrent pericarditis.


Eligibility

Min Age: 18 YearsMax Age: 80 Years

Inclusion Criteria5

  • Phase 2 and 3: Has a diagnosis of recurrent pericarditis
  • Phase 2 and 3: Has signs and symptoms of recurrent pericarditis despite treatment with standard therapies
  • Phase 2 and 3: Weighs at least 40 kg
  • Phase 2: Taking NSAIDS and/or colchicine (in any combination)
  • Phase 3: Taking NSAIDs and/or colchicine and/or glucocorticoids (in any combination)

Exclusion Criteria11

  • Phase 2 and 3: Has a diagnosis of pericarditis that is secondary to specific prohibited etiologies.
  • Phase 2 and 3: Has received an investigational drug during the 4 weeks before screening or is planning to receive an investigational drug at any time during the study.
  • Phase 2 and 3: Has a history of active or untreated, latent tuberculosis (TB) prior to screening.
  • Phase 2 and 3: Has a history of immunodeficiency.
  • Phase 2 and 3: Has a history of immunosuppression, including positive human immunodeficiency virus (HIV) test results.
  • Phase 2 and 3: Has chest x-ray at Screening or within 12 weeks before first study drug administration, with evidence of malignancy, abnormality consistent with prior or active TB infection or active infection.
  • Phase 2 and 3: Has a history of malignancy of any organ system within the past 5 years before Screening (other than a successfully treated non metastatic cutaneous squamous cell carcinoma or basal cell carcinoma and/or localized carcinoma in situ of the cervix).
  • Phase 2 and 3: Has a known or suspected current active infection or a history of chronic or recurrent infectious disease (\> 3 episodes in prior 12 months), including but not limited to, genitourinary infection, chest infection, sinusitis, or skin/soft tissue infection.
  • Phase 2 and 3: Has had a serious infection, has been admitted to the hospital for an infection, or has been treated for a documented infection requiring antibiotics for a documented infection within 2 weeks prior to first study drug administration.
  • Phase 2 and 3: Has had an organ transplant (except corneal transplant performed more than 3 months prior to first study drug administration).
  • Phase 2 and 3: In the Investigator's opinion, has any other medical condition that could adversely affect the subject's participation or interfere with study evaluations.

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Interventions

DRUGKPL-387

administered by subcutaneous injection

DRUGPlacebo

administered by subcutaneous injection


Locations(46)

Investigational Site 018

Gilbert, Arizona, United States

Investigational Site 030

Los Angeles, California, United States

Investigational Site 008

San Francisco, California, United States

Investigational Site 044

Santa Monica, California, United States

Investigational Site 016

Westminster, Colorado, United States

Investigational Site 001

Columbus, Georgia, United States

Investigational Site 004

Chicago, Illinois, United States

Investigational Site 014

Indianapolis, Indiana, United States

Investigational Site 002

Overland Park, Kansas, United States

Investigational Site 043

Baltimore, Maryland, United States

Investigational Site 012

Rochester, Minnesota, United States

Investigational Site 046

Kansas City, Missouri, United States

Investigational Site 015

New York, New York, United States

Investigational Site 022

New York, New York, United States

Investigational Site 009

Cincinnati, Ohio, United States

Investigational Site 003

Cleveland, Ohio, United States

Investigational Site 005

Austin, Texas, United States

Investigational Site 013

Houston, Texas, United States

Investigational Site 042

Burlington, Vermont, United States

Investigational Site 006

Charlottesville, Virginia, United States

Investigational Site 023

Norfolk, Virginia, United States

Investigational Site 045

Richmond, Virginia, United States

Investigational Site 027

Ottawa, Ontario, Canada

Investigational Site 028

Montpellier, France

Investigational Site 021

Paris, France

Investigational Site 036

Pessac, France

Investigational Site 019

Poitiers, France

Investigational Site 037

Toulouse, France

Investigational Site 038

Toulouse, France

Investigational Site 034

Athens, Greece

Investigational Site 039

Nea Ionia, Greece

Investigational Site 032

Voula, Greece

Investigational Site 029

Genoa, Italy

Investigational Site 040

Genoa, Italy

Investigational Site 007

Milan, Italy

Investigational Site 033

Udine, Italy

Investigational Site 041

Varese, Italy

Investigational Site 031

Warsaw, Poland

Investigational Site 025

Belgrade, Serbia

Investigational Site 026

Belgrade, Serbia

Investigational Site 010

Barcelona, Spain

Investigational Site 024

Madrid, Spain

Investigational Site 011

Murcia, Spain

Investigational Site 020

London, United Kingdom

Investigational Site 035

London, United Kingdom

Investigational Site 017

Southampton, United Kingdom

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NCT07010159


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